Pentalogy of Cantrell with Total Ectopia Cordis and a Major Omphalocele—A Case Report

Title: Pentalogy of Cantrell with Total Ectopia Cordis and a Major Omphalocele—A Case Report
Creator: Delgado, Arturo Leonardo
Creator: Matongo, Kopolo Mfuneko
Creator: Dumo, Bangasa
Creator: Mzayiya, Ntsikelelo
Creator: Mrara, Busisiwe
Subject: Ectopia cordis, major omphalocele, sternum agenesis, anterior diaphragmatic deficiency, absence of pericardium, persistence of the Ductus arteriosus.
Date: 2019
Type: Journal Article
Identifier: http://hdl.handle.net/11260/6360
Identifier: vital:45379
Description: Abstract: Ectopia cordis (EC) is a rare malformation due to failure of maturation of the midline mesodermal components of the chest and abdomen. It can be defined as 0.1% of congenital heart diseases, and it could present isolated or could belong to the spectrum of the Pentalogy of Cantrell (PoC), which is a rare congenital disorder first described in 1958 by Cantrell.We are reporting a rare case of total ectopia cordis, associated to a major omphalocele, total agenesis of the sternum, anterior diaphragmatic deficiency, absence of pericardium, and persistence of the Ductus arteriosus, making therefore these features compatible with a full spectrum of the Pentalogy of Cantrell, encouraging us to report this case.
Format: Pdf
Publisher: David Publishing
Language: English
Rights: Journal of Pharmacy and Pharmacology

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